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Most children are born with two ventricles that pump blood to the lungs and the body. Complex single ventricle is a term that describes a group of rare heart defects in which the heart has a single main pumping chamber (ventricle) that performs the work of both ventricles, having to pump blood to both the lungs and body. Without surgery, most children with single ventricles will not survive to their first birthday.
Complex single ventricle defects include:
A complex single ventricle repair is tailored to the type of defect and many other factors. It takes experience, skill and training to match the right treatment with your child’s unique condition.
Norton Children’s Heart Institute has a network of remote diagnostic and treatment services in Kentucky and Southern Indiana. Our specialists at Norton Children’s Heart Institute will be able to identify a treatment plan that is specially designed for your child’s type of complex single ventricle.
Norton Children’s Heart Institute, affiliated with the UofL School of Medicine, is the leading provider of pediatric heart care in Louisville and Southern Indiana.
A complex single ventricle defect is a serious heart condition that causes one ventricle of the heart to have to do the workload of two ventricles. Patients also have lower oxygen levels than expected. A child with a complex single ventricle may need two or three heart surgeries during the first three years of life.
The overall goal of the surgeries is to separate the body’s two circulation paths, allowing the child’s oxygen saturation to become normal, or as close to normal as possible. After all repair stages are completed, the patient’s single ventricle will pump blood to the body and blood will passively return to the lungs without the use of a “right-sided” ventricle.
Depending on a child’s specific condition, the following procedures may be used:
After having the procedures that separate the two body’s circulations, oxygen saturation levels in the blood will become normal or near normal. However, these patients are still left with a single-ventricle heart. This means the heart will have difficulty pumping the amount of blood the body needs (cardiac output). Children with a single ventricle can live active and eventful lives, but they may not be able to exert themselves like children with two ventricles.
A child who has had a complex single ventricle defect repaired will need lifelong care with a cardiologist. The cardiologist will look for developing complications and issues over time, such as abnormal heart rhythms or congestive heart failure. Because they have only one ventricle, these patients are at risk for heart failure early in life and may need to be treated with various medications, or even a heart transplant if their heart failure is severe.