Cystic Fibrosis-Related Diabetes

Cystic fibrosis-related diabetes (CFRD) is a unique kind of diabetes that affects people with cystic fibrosis. The pediatric endocrinologists with Norton Children’s Endocrinology, affiliated with the UofL School of Medicine, and the Wendy Novak Diabetes Center work alongside Norton Children’s pulmonologists to provide individualized treatment plans to help children with cystic fibrosis (CF) manage their CFRD.

What is cystic fibrosis-related diabetes?

CFRD shares some characteristics of both Type 1 and Type 2 diabetes. Children with CF experience a thick and sticky mucus that clogs up tubes, ducts and passageways in different organs. This mucus can cause the pancreas to scar, preventing it from producing insulin as it should. This causes children with CF to become insulin deficient like children with Type 1 diabetes.

The pancreas may still make insulin, but not at healthy levels. Children with CFRD may be insulin resistant like people with Type 2 diabetes. This means that they do to respond to insulin the way people without diabetes do, which causes high levels of glucose (sugar) in the blood. While CFRD has similarities to Type 1 and Type 2 diabetes, the treatment and management of CFRD is different.

CFRD Diagnosis

Children with CF who are age 8 and older should be screened for CFRD every year through an oral glucose tolerance test (OGTT). An OGTT is a two-hour test that checks blood sugar levels before and after drinking a sweet drink. The OGTT is the best way of diagnosing CFRD because the traditional hemoglobin A1c (HbA1c) test often used to diagnose other types of diabetes often is normal in children with CF.

CFRD Treatment

The board-certified, fellowship-trained endocrinologists with Norton Children’s and UofL work to provide an individualized plan for your child to manage CFRD.

The Wendy Novak Diabetes Center team works alongside other Norton Children’s specialists, including pulmonologists, to help you and your child manage CF and CFRD by:

  • Providing nutritional guidance to help your child gain and maintain a healthy weight. Children with CFRD need a diet that addresses both their CF and their CFRD, and our registered dietitians and diabetes educators can create a unique plan for your child.
  • Monitoring blood sugar and adjusting insulin therapy to keep blood sugar levels stable to avoid complications
Endocronology

Norton Children’s Endocrinology

Specialized children’s endocrinology care
Call (502) 588-3400

Transforming endocrinology care into one of the best in the nation

Since Louisville native and endocrinologist Kupper A. Wintergerst, M.D., arrived at Norton Children’s Hospital in 2006, he has expanded the endocrinology and diabetes program from a single physician and nurse practitioner to 10 physicians and […]

Read Full Story

Dehydration symptoms in kids and what parents can do

The early hot days of summer can mean getting caught off guard by heat-related illnesses, such as dehydration, heat cramps, heat exhaustion and heatstroke. The Centers for Disease Control and Prevention estimates that in the […]

Read Full Story

Diabetes-friendly recipes: Hummus or guacamole roll-ups

GUACAMOLE ROLL-UPS Ingredients: 4 whole-wheat tortillas 1 cup Simple Truth traditional guacamole, 1/4 cup per tortilla 3 to 4 pieces sliced turkey or ham Shredded lettuce 3 to 4 Roma tomatoes, diced Shredded low-fat cheese, […]

Read Full Story

Can my child with diabetes take medicine for a cold?

When your child is sick, you want to do everything you can to help him or her feel better. The cold-and-flu aisle can be a minefield for parents of children with Type 1 or Type […]

Read Full Story

Recipe: Easy trail mix

Having healthy snacks available can be crucial for families on the go with a child with diabetes. You can make this easy trail mix ahead of time and portion for single 1-ounce servings for a […]

Read Full Story
Related Stories

Transforming endocrinology care into one of the best in the nation

Since Louisville native and endocrinologist Kupper A. Wintergerst, M.D., arrived at Norton Children’s Hospital in 2006, he has expanded the endocrinology and diabetes program from a single physician and nurse practitioner to 10 physicians and […]

Read Full Story

Dehydration symptoms in kids and what parents can do

The early hot days of summer can mean getting caught off guard by heat-related illnesses, such as dehydration, heat cramps, heat exhaustion and heatstroke. The Centers for Disease Control and Prevention estimates that in the […]

Read Full Story

Diabetes-friendly recipes: Hummus or guacamole roll-ups

GUACAMOLE ROLL-UPS Ingredients: 4 whole-wheat tortillas 1 cup Simple Truth traditional guacamole, 1/4 cup per tortilla 3 to 4 pieces sliced turkey or ham Shredded lettuce 3 to 4 Roma tomatoes, diced Shredded low-fat cheese, […]

Read Full Story

Can my child with diabetes take medicine for a cold?

When your child is sick, you want to do everything you can to help him or her feel better. The cold-and-flu aisle can be a minefield for parents of children with Type 1 or Type […]

Read Full Story

Recipe: Easy trail mix

Having healthy snacks available can be crucial for families on the go with a child with diabetes. You can make this easy trail mix ahead of time and portion for single 1-ounce servings for a […]

Read Full Story

Search our entire site.